MMA/PA express
Indications
A methionine, threonine, and valine free and isoleucine low protein substitute for use in the dietary management of Methylmalonic Acidaemia (MMA) and Propionic Acidaemia (PA) in individuals aged 8 years and older.
Product Features
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Methionine, threonine, valine free
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Low isoleucine content
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Low volume
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Contains the necessary mixture of amino acids, carbohydrates, minerals, trace elements and vitamins to meet the daily nutritional needs of this age group
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Provides 60g of protein equivalent per 100g of powder
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Unflavored powder with separate FlavourPac sachets available
Nutritional Information & Ingredients
Available at the end of this page.
Important Information
MMA/PA express must only be given to patients with proven Methylmalonic Acidaemia or Propionic Acidaemia and under strict medical supervision. It is not recommended for children under 8 years of age or as a sole source of nutrition. The product does contain a source of phenylalanine. MMA/PA express is not for parenteral use.
Dosage and Administration
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Dosage of MMA/PA express should be determined by the clinician or dietitian
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The daily protein requirement is given as MMA/PA express (100g is equivalent to 60g of protein).
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Additional protein is provided from natural protein sources in medically prescribed quantities to provide methionine, threonine, valine and isoleucine in controlled amounts, which is essential for normal development.
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Foods high in carbohydrate and fat but low in protein should be provided as an energy source to supply the remainder of daily calories.
Guidelines for Preparation and Use
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Empty the contents of a sachet into a beaker (provided), and add a FlavourPac sachet if desired. Add cold water to about half way up the beaker (approximately 80ml). Secure the lid and shake for 10 seconds. Serve and drink immediately.
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Water or permitted drinks should be taken after the MMA/PA express.
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Cover and refrigerate any unused formula. Use prepared formula within 24 hours. Shake well before serving.
Storage
Store unopened sachets at room temperature. After opening, store tightly sealed sachet in a cool, dry place and use within one month. Avoid storing product in areas of extreme temperatures.
Availability
| Product Number | Description | Packaging | NDC Format Code |
| 054371 |
MMA PA express unflavored |
30 x 25g sachets |
50600-0543-71 |
HCPCS: B4155
WIC APPROVED